isovalericacidemia

isovalericacidemia definition - medical

i·so·va·le·ric·ac·i·de·mi·a (īˌsō-və-lîrˌĭ-kăsˌĭ-dēˈmē-ə, -lĕrˌ-)

noun
An inherited disorder of leucine metabolism marked by excessive production of isovaleric acid upon protein ingestion or during infectious episodes and resulting in severe metabolic acidosis.

The American Heritage® Medical Dictionary Copyright © 2009 by Houghton Mifflin Harcourt Publishing Company. Published by Houghton Mifflin Harcourt Publishing Company. All rights reserved.

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